Pulmonary Hypertension ICD-10 Codes: What You Need to Know


A medical condition known as pulmonary hypertension happens when the blood pressure in the pulmonary arteries increases more than usual.

This phenomenon can cause several issues that impair the heart’s capacity to pump blood effectively. The effects of pulmonary hypertension for research and healthcare make it clear how important it is to understand and code for it appropriately.

ICD-10 Codes for Pulmonary Hypertension

Certainly! Here are some ICD-10 codes related to PH :

  1. I27.0 – Primary Pulmonary Hypertension
    • When pulmonary hypertension is recognized as the primary condition and is not associated with any other diseases, this code is used.
  2. I27.1 – Kyphoscoliotic Heart Disease
    • indicates signs of PH associated with kyphoscoliosis, a condition that combines heart disease with spinal deformities.
  3. I27.21 – Pulmonary Hypertension Due to Left Heart Disorder
    • used when a specific left heart condition, such as heart failure, is the cause of PH.
  4. I27.22 – PH Due to Lung Diseases and Hypoxia
    • Useful in cases when low oxygen levels (hypoxia) or lung diseases are the cause of PH.
  5. I27.23 – PH Due to Chronic Pulmonary Embolism
    • indicates that a blood clot in the lung, known as a chronic pulmonary embolism, is the cause of pulmonary hypertension.
  6. I27.24 – Chronic Thromboembolic PH
    • Code specific to cases in which PH is caused by chronic thromboembolic events.
  7. I27.29 – Other Secondary PH
    • covers secondary pulmonary hypertension cases that aren’t classified under any other specific categories.
  8. I27.81 – Cor Pulmonale (Chronic)
    • This code is used to treat chronic cor pulmonale, a condition where lung illnesses affect the right side of the heart.
  9. I27.89 – Other Specified Pulmonary Heart Diseases
    • Useful in cases where the pulmonary heart disease is not included under one of the previously mentioned categories.
  10. I27.9 – Pulmonary Heart Disease, Unspecified
    • Used in cases where the specific type of pulmonary heart disease is unspecified or unidentified.

ICD-10 Code Structure for Pulmonary Hypertension

There is a systematic pattern in the ICD-10 code structure for PH. Alphanumeric characters compose each code, which contains extensive details about the condition. Here’s an overview of the structure:

  1. Character 1 (First Alphanumeric):
    • This character is usually an alphabetical letter (‘I’ or ‘D,’ indicating whether the code is for a neoplasm (‘D’) or an infectious or parasitic disease (‘I’). The letter for PH is ‘I’ since it is known as a circulatory system disease.
  2. Characters 2 and 3 (Numeric):
    • These two characters offer additional categorization. PH is denoted by the code ’27,’ which stands for circulatory system illnesses.
  3. Character 4 (Alphanumeric):
    • This character indicates the disease’s category. The first digit for PH is ‘I27,’ denoting pulmonary heart disorders.
  4. Characters 5 and 6 (Numeric):
    • More specific details regarding the illness are given by these characters. When it regarding pulmonary hypertension, certain codes may be used, such as ‘0’ for primary pulmonary hypertension or ‘1’ for kyphoscoliotic heart disease.
  5. Characters 7 and 8 (Numeric):
    • These characters could provide more details about the condition or its cause. For example, in certain circumstances, ’21’ may represent pulmonary hypertension caused by left heart disease, and ’22’ may represent PH caused by hypoxia and lung disorders.
  6. Characters 9 and 10 (Numeric):
    • These characters are used to give additional information or to be more specific. For example, the ’81’ in ‘I27.81’ indicates a particular type of pulmonary heart disease called chronic cor pulmonale.
  7. Character 11 (Alphanumeric):
    • Currently, this character isn’t used for most codes and is kept for potential future expansion.

Specific ICD-10 Codes for Different Types of PH


Pulmonary Hypertension ICD-10 Codes: What You Need to Know

Here are specific ICD-10 codes for different types of PH :

  1. Primary PH :
    • I27.0
  2. Kyphoscoliotic Heart Disease-Related Pulmonary Hypertension:
    • I27.1
  3. PH Due to Left Heart Disease:
    • I27.21
  4. Pulmonary Hypertension Due to Lung Disease and Low Oxygen:
    • I27.22
  5. PH Due to Chronic Pulmonary Embolism:
    • I27.23
  6. Chronic Thromboembolic Pulmonary Hypertension:
    • I27.24
  7. Other Secondary Pulmonary Hypertension:
    • I27.29
  8. Cor Pulmonale (Chronic):
    • I27.81
  9. Other Specified Pulmonary Heart Diseases:
    • I27.89
  10. Pulmonary Heart Disease, Unspecified:
    • I27.9

Using ICD-10 Codes for Pulmonary Hypertension Billing and Documentation

ICD-10 codes must be utilized properly for billing and documenting pulmonary hypertension to give regulators, insurers, and healthcare providers an accurate picture of the disease. Using these codes correctly is crucial for accurate invoicing, and payment, and to maintain thorough patient records. Let’s explore how ICD-10 codes play a pivotal role in PH billing and documentation:

  1. Accurate Identification and Classification:
    • Medical professionals can effectively identify and categorize multiple types of pulmonary hypertension with the use of ICD-10 codes. To give patients the proper care and develop a full understanding of the particular condition being treated, this accuracy is important.
  2. Billing Accuracy and Reimbursement:
    • Accurate billing is directly impacted by proper coding. ICD-10 codes are specific to each kind of pulmonary hypertension, allowing medical professionals to bill for services associated with the particular illness being treated. Additionally, quick insurance company reimbursement is made possible by accurate coding.
  3. Documentation of Coexisting Conditions:
    • It is typical for PH to coexist with other medical conditions. Healthcare providers can record these comorbidities and provide an extensive overview of the patient’s health status by using the relevant ICD-10 codes. A patient-centered approach to care requires accurate records.
  4. Facilitating Research and Statistics:
    • ICD-10 codes should be used consistently to ensure that health data and research are accurate. Coded data is used by researchers and public health experts to examine patterns, occurrences, and consequences associated with pulmonary hypertension. Also, we are better able to understand the condition on a population level.
  5. Ensuring Compliance with Coding Guidelines:
    • adhering to guidelines for coding is essential to following healthcare laws. Healthcare providers can reduce the risk of audits and penalties by adhering to industry standards by using the correct ICD-10 codes for pulmonary hypertension.
  6. Streamlining Administrative Processes:
    • Correct coding is essential to efficient administrative procedures. ICD-10 codes that are correctly documented make it easier to expedite tasks like insurance claims processing and billing. This effectiveness is especially crucial in hectic medical environments.
  7. Communication with Insurers and Payers:
    • Clear and accurate coding improves communication with insurers and payers. It provides standard language that helps insurers understand the nature and severity of a patient’s condition, reduces the chances of claims denials, and facilitates seamless interactions in the reimbursement process.
  8. Long-Term Patient Care Planning:
    • Comprehensive documentation using ICD-10 codes supports the decision to care for long-term patients. It provides a historical record of the patient’s history of Pulmonary Hypertension to support treatment adjustments, disease progression, and ongoing care.


How is the diagnosis of pulmonary hypertension made?

Discover the diagnostic techniques and tests used by medical professionals to correctly diagnose pulmonary hypertension.

Are there effective treatment options available?

Learn about the variety of PH treatment options that are available, ranging from medication to modifications to your lifestyle.

Is it possible to prevent pulmonary hypertension?

Learn about modifications to lifestyle and preventive strategies that can lower the risk of developing pulmonary hypertension.

What are the prospects for those suffering from PH?

Understand the prognostic factors and the long-term outlook for people with pulmonary hypertension.

How can I help a family member who suffers from pulmonary hypertension?

Learn how to help and sympathize with friends or family members who are experiencing PH.

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